Vahlensieck M, Vahlensieck W, Vahlensieck W
Röntgenabteilung, Malteser Krankenhaus, Akademisches Lehrkrankenhaus, Universität Bonn.
Aktuelle Radiol. 1991 Nov;1(6):302-7.
Cystic kidney dysplasias (multicystic kidney disease) are differentiated from hyperplastic and ectatic cystic kidney diseases by means of pathogenesis in order to simplify the common classification. Six cases of cystic kidney dysplasia are reported (1 child and 5 adults) and in a review of the literature diagnostic and therapeutic strategies are discussed. A characteristic radiological sign is the clublike++ deformation of the rudimentary ureter. Nephrectomy is indicated in case of symptoms such as pain, hypertension or recurrent urinary tract infections or in case of atypical cysts with a risk of malignancy.
为简化常见分类，根据发病机制将囊性肾发育异常（多囊肾病）与增生性和扩张性囊性肾病区分开来。报告了6例囊性肾发育异常病例（1例儿童和5例成人），并在文献综述中讨论了诊断和治疗策略。一个典型的放射学征象是发育不全输尿管的杵状++变形。出现疼痛、高血压或反复尿路感染等症状，或存在有恶性风险的非典型囊肿时，建议行肾切除术。
