Bullorsky E O, Shanley C, Napoli J, Stemmelin G, Emery J, Lajous J R
Servicio de Hematología, Hospital Británico, Buenos Aires, Argentina.
Medicina (B Aires). 1991;51(3):241-3.
Thrombotic thrombocytopenic purpura (TTP) is a rare disorder of unknown etiology, clinically characterized by a diagnostic pentad (thrombocytopenia, microangiopathic hemolytic anemia, neurologic signs and symptoms, fever and renal damage). Recent reports in the medical literature have described its association with the human immunodeficiency virus (HIV). We report such a case in a woman admitted with TTP in whom HIV seropositivity was found. The histopathologic findings in biopsies and autopsy confirmed the clinical diagnosis of TTP: disseminated microthrombosis in arterioles and capillaries.
血栓性血小板减少性紫癜(TTP)是一种病因不明的罕见疾病,临床特征为诊断五联征(血小板减少、微血管病性溶血性贫血、神经体征和症状、发热及肾损害)。医学文献中的近期报告描述了它与人类免疫缺陷病毒(HIV)的关联。我们报告了一例因TTP入院的女性病例,该患者HIV血清学检测呈阳性。活检和尸检的组织病理学结果证实了TTP的临床诊断:小动脉和毛细血管内弥漫性微血栓形成。