Templet Julie T, Welsh John Patrick, Cusack Carrie Ann
Center for Sight, Sarasota, Florida, USA.
Cutis. 2007 Dec;80(6):473-6.
Dermatitis herpetiformis (DH) is a chronic pruritic cutaneous eruption associated with gluten-sensitive enteropathy (celiac disease [CD]) and immunoglobulin A (IgA) deposition in the skin. While the disease is not uncommon among adolescents, DH is rarely seen in prepubertal patients. Children with DH present similarly to adults; however, uncommon skin findings have been reported. Because of an increased risk for autoimmune diseases and lymphoma, accurate diagnosis and treatment are imperative. We present a case of DH in a 6-year-old Latino boy previously diagnosed with atopic dermatitis and recurrent urticaria. Our aim is to highlight the various cutaneous presentations of DH and encourage clinicians to consider this diagnosis in young patients with recalcitrant atypical skin disease.
疱疹样皮炎(DH)是一种慢性瘙痒性皮肤疹,与麸质敏感性肠病(乳糜泻[CD])及免疫球蛋白A(IgA)在皮肤中的沉积相关。虽然该疾病在青少年中并不罕见,但在青春期前患者中很少见。患有DH的儿童临床表现与成人相似;然而,也有罕见皮肤表现的报道。由于自身免疫性疾病和淋巴瘤的风险增加,准确的诊断和治疗至关重要。我们报告一例6岁拉丁裔男孩患DH的病例,该男孩之前被诊断为特应性皮炎和复发性荨麻疹。我们的目的是强调DH的各种皮肤表现,并鼓励临床医生在患有顽固性非典型皮肤病的年轻患者中考虑这一诊断。