Hassan Shahid, Abdullah Jafri M, Wan Din Shah Jihan, Idris Zamzuri
Department of ORL-HNS, School of Medical Sciences, Health Campus, Universiti Sains Malaysia, Kota Bharu, Kelantan, Malaysia.
J Med Case Rep. 2008 Feb 18;2:49. doi: 10.1186/1752-1947-2-49.
Chordoma is a rare malignant tumour with an incidence of metastasis of less than 10 percent. Usually arising from clivus its posterior extension may involve the brainstem before presenting as nasal mass and obstruction. Surgery is the main mode of treatment with adjuvant radiotherapy. However surgery is rarely possible for a large intracranial lesion.
We report the case of an adolescent patient with a chordoma extending posteriorly to the brainstem and anteriorly to the nasopharynx and managed by the combination of resection using a maxillomandibular swing approach and the use of a neurosurgical ultrasonic aspirator.
Maxillomandibular swing approach provides good access for large nasopharyngeal tumour extending brainstem area.
脊索瘤是一种罕见的恶性肿瘤，转移发生率低于10%。通常起源于斜坡，其后部延伸可能在表现为鼻腔肿物和阻塞之前累及脑干。手术是主要的治疗方式并辅以放疗。然而，对于大型颅内病变，手术很少可行。
我们报告了一例青少年患者，其脊索瘤向后延伸至脑干，向前延伸至鼻咽部，采用上颌下颌摆动入路切除联合神经外科超声吸引器进行治疗。
上颌下颌摆动入路为延伸至脑干区域的大型鼻咽肿瘤提供了良好的手术入路。
