Matsumoto J, Towbin R B, Ball W S
Department of Radiology, Children's Hospital Medical Center, Cincinnati, Ohio.
Pediatr Radiol. 1989;20(1-2):28-32. doi: 10.1007/BF02010629.
Cranial chordomas are uncommon, accounting for less than 1% of all intracranial neoplasms. Although they are presumed to arise from congenital notochordal remnants, it is rare for these tumors to present in childhood. Only 35 cases of cranial chordomas have been reported in children 16 years of age or younger. We report 2 additional cases of pediatric cranial chordomas. One occurred in a 4 month old infant and to our knowledge represents the earliest age of presentation yet reported. The second case documents the value of MR imaging in delineating the extent of the tumor and defining its relationship to adjacent structures.
颅底脊索瘤并不常见，占所有颅内肿瘤的比例不到1%。尽管推测它们起源于先天性脊索残余，但这些肿瘤在儿童期出现的情况很少见。16岁及以下儿童中仅报道过35例颅底脊索瘤。我们报告另外2例儿童颅底脊索瘤病例。1例发生在一名4个月大的婴儿身上，据我们所知，这是迄今报道的最早发病年龄。第二例病例证明了磁共振成像在描绘肿瘤范围及其与相邻结构关系方面的价值。
