Baloch M S, Fitzwilliams B, Mellerio J, Lakasing L, Bewley S, O'Sullivan G
Department of Anaesthetics, St Thomas' Hospital, London, UK.
Int J Obstet Anesth. 2008 Apr;17(2):153-8. doi: 10.1016/j.ijoa.2007.04.008. Epub 2008 Mar 4.
Dystrophic epidermolysis bullosa is an inherited severe bullous condition characterised by extreme skin fragility and blistering in response to minor trauma. We present two obstetric cases with recessive dystrophic epidermolysis bullosa, one who underwent elective caesarean section, the other who delivered vaginally. The key points in the anaesthetic management of the obstetric patient with dystrophic epidermolysis bullosa include multidisciplinary preassessment, airway management strategies and the role of regional anaesthesia.
营养不良性大疱性表皮松解症是一种遗传性严重大疱性疾病,其特征是皮肤极度脆弱,轻微创伤即可引起水疱。我们报告两例隐性营养不良性大疱性表皮松解症的产科病例,一例接受择期剖宫产,另一例经阴道分娩。患有营养不良性大疱性表皮松解症的产科患者麻醉管理的关键点包括多学科术前评估、气道管理策略以及区域麻醉的作用。