Shah Nidhi, Kumaraswami Sangeeta, Mushi Juliet E
Department of Obstetrics & Gynecology, New York Medical College, Westchester Medical Center, 100, Woods Road, Valhalla, New York 10595, USA.
Department of Anesthesiology, New York Medical College, Westchester Medical Center,100,Woods Road, Valhalla, New York 10595,USA.
Case Rep Womens Health. 2019 Sep 5;24:e00140. doi: 10.1016/j.crwh.2019.e00140. eCollection 2019 Oct.
Epidermolysis bullosa (EB) encompasses a group of diseases characterized by extreme fragility of skin and mucous membranes, resulting in blister formation following minimal injury. There are 4 types of EB, with epidermolysis bullosa simplex (EBS) being the most common. We report our experience with the care of a parturient woman diagnosed with EBS. There is little literature on pregnancy in women with this condition. Special precautions are necessary during diagnostic and therapeutic interventions to avoid bullae formation or exacerbation of existing lesions. Frictional or shearing forces are typically more damaging than compressive forces. Multidisciplinary planning was done for our patient to ensure uneventful labor and delivery. Elective induction of labor was started at 40 weeks of gestation. She eventually underwent a cesarean delivery after failed trial of labor. We present this case to highlight the obstetric and anesthetic implications of caring for a parturient with EBS.
大疱性表皮松解症（EB）是一组以皮肤和黏膜极度脆弱为特征的疾病，轻微损伤后即可形成水疱。EB有4种类型，其中单纯性大疱性表皮松解症（EBS）最为常见。我们报告了对一名诊断为EBS的产妇的护理经验。关于患有这种疾病的女性怀孕的文献很少。在诊断和治疗干预期间，需要采取特殊预防措施以避免水疱形成或现有病变加重。摩擦或剪切力通常比压力更具破坏性。我们为患者进行了多学科规划，以确保分娩顺利。妊娠40周时开始择期引产。试产失败后，她最终接受了剖宫产。我们展示这个病例以突出护理患有EBS的产妇的产科和麻醉方面的问题。
