Haresh K P, Prabhakar R, Anand Rajan K D, Sharma D N, Julka P K, Rath G K
Department of Radiotherapy and Oncology, All India Institute of Medical Sciences, Ansari Nagar, New Delhi 110 029, India.
Pituitary. 2009;12(3):276-9. doi: 10.1007/s11102-008-0099-1.
Sellar paragangliomas are very rare lesions with only 11 previous cases described in the literature. We present a further case of sellar paraganglioma. The patient is a 17-year-old man who developed headache, visual blurring, and diplopia. MRI showed a sellar lesion. Trans-nasal trans-sphenoid biopsy showed features of paraganglioma. He was treated by Stereotactic radiotherapy. Four months after treatment he developed bone metastases which was palliated by radiation, zoledronic acid, and chemotherapy. This is the first case of sellar paraganglioma showing metastases to bone.
鞍区副神经节瘤是非常罕见的病变,文献中仅描述过11例既往病例。我们报告了1例鞍区副神经节瘤的新病例。患者为一名17岁男性,出现头痛、视力模糊和复视症状。磁共振成像(MRI)显示鞍区有一个病变。经鼻蝶窦活检显示为副神经节瘤特征。他接受了立体定向放射治疗。治疗4个月后,他出现了骨转移,通过放疗、唑来膦酸和化疗得以缓解。这是首例出现骨转移的鞍区副神经节瘤病例。