Macedo A, Paixão A, Lima M, Sampayo F
Serviço de Cardiologia Pediátrica Hospital de Santa Marta, Lisboa.
Rev Port Cardiol. 1991 Jul-Aug;10(7-8):581-5.
A case of atrial septal defect in association with dilated cardiomyopathy is presented. Evolutive features are mainly assessed by echocardiography. On initial presentation the findings on physical examination pointed to the diagnosis of atrial septal defect with severe congestive heart failure. In addition to the demonstration of the congenital heart disease, echocardiography showed very dilated right atrial and ventricular cavities and later appearance of right atrium intracavitary thrombi. Left cavities were initially normal but, after surgical repair of the atrial septal defect, they rapidly increased. Endomyocardial biopsy confirmed the diagnosis of cardiomyopathy, which clinically seemed to only affect the right ventricle, but actually shown to be a diffuse myocardial disease.
本文报告一例房间隔缺损合并扩张型心肌病的病例。主要通过超声心动图评估其演变特征。初次就诊时，体格检查结果提示为房间隔缺损合并严重充血性心力衰竭。除了证实先天性心脏病外，超声心动图显示右心房和心室腔非常扩张，随后右心房腔内出现血栓。左心腔最初正常，但在房间隔缺损手术修复后迅速增大。心内膜活检证实为心肌病，临床上似乎仅累及右心室，但实际上是一种弥漫性心肌疾病。
