Suri Deepti, Sodhi Kushaljit S, Muralidharan Jayashree, Manoj Rohit, Singhi Sunit
Department of Pediatrics, Advanced Pediatrics Centre, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Pediatr Emerg Care. 2008 Mar;24(3):164-6. doi: 10.1097/PEC.0b013e3181668aff.
Scimitar syndrome is a rare congenital anomaly characterized by total or partial anomalous venous drainage of the right lung to the inferior vena cava. The infantile form presents with congestive heart failure and respiratory distress in early months of life. We report here the case of a 6-month-old male child who presented with second episode of respiratory distress and wheeze. Poor response to bronchodilators led to fibreoptic bronchoscopy and computed tomographic scan that revealed bronchial anomalies with aberrant drainage of right lung into the inferior vena cava by scimitar vein. The case illustrates that one of the rare causes of wheezing in an infant could be scimitar syndrome.
弯刀综合征是一种罕见的先天性异常,其特征为右肺全部或部分静脉血异常引流至下腔静脉。婴儿型在出生后数月内表现为充血性心力衰竭和呼吸窘迫。我们在此报告一例6个月大男童,他出现了第二次呼吸窘迫和喘息发作。对支气管扩张剂反应不佳,随后进行了纤维支气管镜检查和计算机断层扫描,结果显示存在支气管异常,右肺通过弯刀静脉异常引流至下腔静脉。该病例表明,婴儿喘息的罕见原因之一可能是弯刀综合征。