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左三房心合并右肺静脉部分异位引流。病例报告。

Association of a Cor Triatriatum Sinister and a right partial anomalous pulmonary venous return. A case report.

作者信息

Tueche S G, Demanet H, Goldstein J P, Dessy H, Viart P, Deuvaert F E

机构信息

Department of Cardiac Surgery, Brugmann University Hospital, Brussels, Belgium.

出版信息

Acta Chir Belg. 2005 Apr;105(2):217-8.

PMID:15906920
Abstract

A 56-day old baby girl referred for recurrent respiratory tract infections and stridor, showed a rare association of a Cor Triatriatum Sinister (CTS) and a right Partial Anomalous Pulmonary Venous Return (PAPVR), in the form of a stenosed Scimitar vein, draining the right pulmonary veins to the subdiaphragmatic inferior vena cava (IVC), on echography and angiography. The baby underwent successful surgical repair of the CTS, by resection of the obstructive false membrane and reconnection of the Scimitar vein to the left atrium. At the age of 5 years, the child is doing well without any evidence of obstruction on the right or the left pulmonary venous drainage.

摘要

一名56天大的女婴因反复呼吸道感染和喘鸣前来就诊,经超声心动图和血管造影检查发现,她患有罕见的左房三房心(CTS)合并右肺部分异常静脉回流(PAPVR),表现为一条狭窄的弯刀状静脉,将右肺静脉引流至膈下下腔静脉(IVC)。该婴儿接受了成功的CTS手术修复,切除了阻塞性假膜,并将弯刀状静脉重新连接至左心房。5岁时,患儿情况良好,左右肺静脉引流均无阻塞迹象。

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