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经血管内治疗不可切除的腹膜后平滑肌肉瘤侵犯所致急性破裂腹主动脉。

Endovascular treatment of an acutely ruptured abdominal aorta from tumor invasion by an unresectable retroperitoneal leiomyosarcoma.

作者信息

Stambo Glenn, Valentin Marlene, Kerr Thomas M, Blanco Raphael

机构信息

SDI Radiologists, St. Joseph's Hospital and Medical Center, Tampa, FL, USA.

出版信息

Ann Vasc Surg. 2008 Jul-Aug;22(4):568-70. doi: 10.1016/j.avsg.2007.11.004. Epub 2008 Mar 25.

DOI:10.1016/j.avsg.2007.11.004
PMID:18367373
Abstract

Retroperitoneal leiomyosarcomas account for <1% of all tumors diagnosed in the U.S. They are usually unresectable at the time of diagnosis due to their vague clinical presentation. Aortic rupture from tumor invasion by retroperitoneal leiomyosarcomas is extremely rare and has only been described in one case report. We describe a case of an unresectable retroperitoneal leiomyosarcoma eroding into the infrarenal abdominal aorta resulting in an acute contained intratumoral hemorrhage successfully treated with a percutaneous placed abdominal aortic endograft. This article discusses the endovascular treatment of this rare medical emergency performed quickly and effectively in our endovascular suite. Endovascular specialists should be familiar with this lifesaving endovascular option in the setting of an acute aortic rupture.

摘要

腹膜后平滑肌肉瘤占美国所有确诊肿瘤的比例不到1%。由于其临床表现模糊,通常在诊断时无法切除。腹膜后平滑肌肉瘤侵袭导致主动脉破裂极为罕见,仅有一篇病例报告对此进行过描述。我们报告一例无法切除的腹膜后平滑肌肉瘤侵蚀肾下腹主动脉,导致急性肿瘤内局限性出血,经皮置入腹主动脉内支架成功治疗的病例。本文讨论了在我们的血管腔内治疗室快速有效地对这种罕见医疗急症进行血管腔内治疗的情况。血管腔内治疗专家应熟悉在急性主动脉破裂情况下这种挽救生命的血管腔内治疗方法。

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Endovascular treatment of an acutely ruptured abdominal aorta from tumor invasion by an unresectable retroperitoneal leiomyosarcoma.经血管内治疗不可切除的腹膜后平滑肌肉瘤侵犯所致急性破裂腹主动脉。
Ann Vasc Surg. 2008 Jul-Aug;22(4):568-70. doi: 10.1016/j.avsg.2007.11.004. Epub 2008 Mar 25.
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Abdominal aortic invasion by leiomyosarcoma.平滑肌肉瘤侵犯腹主动脉。
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Massive intraabdominal bleeding due to a retroperitoneal leiomyosarcoma.腹膜后平滑肌肉瘤导致的大量腹腔内出血。
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Images in Vascular Medicine. Multivessel obstruction and treatment in a patient with retroperitoneal leiomyosarcoma.血管医学影像。一名腹膜后平滑肌肉瘤患者的多血管阻塞及治疗
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