Sokullu Onur, Sanioglu Soner, Deniz Hayati, Ayoglu Umut, Ozgen Ayca, Bilgen Fuat
Department of Cardiovascular Surgery, Siyami Ersek Thoracic and Cardiovascular Surgery Training and Research Hospital, Istanbul, Turkey.
Heart Surg Forum. 2008;11(2):E117-9. doi: 10.1532/HSF98.20071176.
Rhabdomyosarcoma is a rare malignant tumor of the heart that accounts for 20% of all primary malignant neoplasms of the heart. Symptoms vary in accordance with the location of the mass; unfortunately, by the time the patient becomes symptomatic, the tumor has already metastasized to other organs. Diagnosis is frequently obtained via transthoracic or transesophageal echocardiography and nuclear magnetic resonance imaging. Surgery is indicated for malignant cardiac neoplasms to relieve cardiac symptoms and to prolong patient survival. Subsequent postoperative chemotherapy or radiotherapy is necessary, and the long-term prognosis is poor. We present a case of a primary cardiac rhabdomyosarcoma that arose from the lateral wall of the right atrium and required implantation of a permanent cardiac pacemaker after surgery.
横纹肌肉瘤是一种罕见的心脏恶性肿瘤,占所有原发性心脏恶性肿瘤的20%。症状因肿块位置而异;不幸的是,当患者出现症状时,肿瘤已经转移到其他器官。诊断通常通过经胸或经食管超声心动图以及核磁共振成像来进行。对于恶性心脏肿瘤,手术的目的是缓解心脏症状并延长患者生存期。术后随后的化疗或放疗是必要的,且长期预后较差。我们报告一例原发性心脏横纹肌肉瘤病例,该肿瘤起源于右心房侧壁,术后需要植入永久性心脏起搏器。