Fan Hong-Guang, Meng Jian, Pan Shi-Wei, Zheng Zhe, Hu Sheng-Shou
Department of Cardiovascular Surgery, Cardiovascular Institute and Fu-Wai Heart Hospital, CAMS and PUMC, 167 Beilishi Road, Beijing, China.
J Card Surg. 2009 Jul-Aug;24(4):480-2. doi: 10.1111/j.1540-8191.2009.00837.x.
We present a case report of a 48-year-old man with a huge left atrial rhabdomyosarcoma who presented as severe mitral stenosis and accepted emergency surgery. Two years later, a pathologic fracture revealed osseous metastasis, and intracardiac recurrence was detected by echocardiography. The patient died of multiple organ failure in the end. This case is an unusual presentation of complete course of cardiac rhabdomyosarcoma (CR) from diagnosis, operation, recurrence, and metastasis to death. Although primary CR is highly lethal, operation should be indicated to clarify the diagnosis, relieve symptoms, and improve short-term survival.
我们报告一例48岁男性巨大左房横纹肌肉瘤病例,该患者表现为严重二尖瓣狭窄并接受了急诊手术。两年后,病理性骨折提示骨转移,超声心动图检查发现心脏内复发。患者最终死于多器官功能衰竭。该病例是心脏横纹肌肉瘤(CR)从诊断、手术、复发、转移直至死亡的完整病程的罕见表现。尽管原发性CR致死率很高,但仍应进行手术以明确诊断、缓解症状并提高短期生存率。