Yalniz E, Alicioglu B, Benlier E, Yilmaz B, Altaner S
Department of Orthopaedic Surgery, Trakya University School of Medicine, Edime,Turkey.
JBR-BTR. 2008 Jan-Feb;91(1):14-7.
Gorham-Stout disease is characterized by local proliferation of small vascular or lymphatic channels resulting in progressive destruction and resorption of bone. The etiology and pathogenesis of the disease remains mostly unknown, despite some 175 reported cases. A case of Gorham-Stout disease of the humerus in a 14-year-old boy is described. The patient presented with progressive pain and deformity of the right arm. Although the disease was described in different bones of the body its location in the humerus is rare. We report the natural history and clinical follow-up in a young patient. A fibular graft was performed but 10 months later, resorption and pathological fractures occurred again. This study presents the radiographic and MRI features of Gorham disease.
戈勒姆-斯托特病的特征是小血管或淋巴管局部增生，导致骨质进行性破坏和吸收。尽管已有约175例报道病例，但该病的病因和发病机制大多仍不清楚。本文描述了一名14岁男孩肱骨戈勒姆-斯托特病的病例。该患者表现为右臂进行性疼痛和畸形。尽管该病在身体不同骨骼中均有描述，但其位于肱骨的情况较为罕见。我们报告了一名年轻患者的自然病史和临床随访情况。进行了腓骨移植，但10个月后，再次出现吸收和病理性骨折。本研究展示了戈勒姆病的影像学和MRI特征。
