Noman Sana, Faiz Seema, Khan Sohail Ahmed, Sattar Amjad
Department of Radiology, Dow Institute of Radiology, Dow University of Health Sciences, Karachi.
J Coll Physicians Surg Pak. 2018 Sep;28(9):S164-S165. doi: 10.29271/jcpsp.2018.09.S164.
Gorham-Stout disease is a rare disease characterised by endothelial proliferation of lymphatics and vessels. It is also known as vanishing bone disease. Increased vascularity and proliferation lead to progressive bony osteolysis. We report a case of a 17-year female diagnosed as having post traumatic Gorham-Stout disease. Being reported for the first time from our population, this will be an informative addition to the already available literature. On X-rays, initially there is osteopenia with patchy distribution followed by coalescence of osteopenic patches, erosion of cortex with soft tissue involvement, and finally bone resorption. MRI shows increased T2 signal with heterogeneous enhancement.
戈勒姆-斯托特病是一种罕见疾病，其特征为淋巴管和血管的内皮细胞增生。它也被称为骨质消失症。血管增多和增生导致进行性骨质溶解。我们报告一例17岁女性被诊断为创伤后戈勒姆-斯托特病的病例。这是首次在我们的人群中报道，将为已有文献增添有价值的内容。X线检查最初表现为骨质减少，呈斑片状分布，随后骨质减少区融合，皮质侵蚀并累及软组织，最终出现骨质吸收。磁共振成像显示T2信号增强，强化不均匀。
