Hong Seong Bin, Kim Cheol-Woo, Kim Ji Hye, Kim Jun Sig, Han Seung Baik
Department of Internal Medicine, College of Medicine, Inha University, Incheon, South Korea.
J Emerg Med. 2011 Nov;41(5):e99-e101. doi: 10.1016/j.jemermed.2008.04.004. Epub 2008 May 16.
Angioedema due to acquired C1 esterase deficiency is a rare condition and a non-inflammatory disease characterized by episodes of edema of the mucosa of the upper airway or gastrointestinal tract. The purpose of this case report is to heighten awareness among emergency physicians of a peritonitis-like condition that can develop into angioedema due to acquired C1 esterase inhibitor deficiency, and thereby help to prevent false diagnosis resulting in unnecessary surgical intervention. We report the case of a 21-year-old man who presented to the Emergency Department (ED) with abdominal pain. He was later diagnosed with angioedema of the gastrointestinal tract due to acquired C1 esterase deficiency that was initially suspected as peritonitis. Careful evaluation of the acute abdomen in acquired C1 esterase deficiency is very important in the ED to distinguish between medical and surgical causes of an acute abdomen.
获得性C1酯酶缺乏所致血管性水肿是一种罕见的非炎症性疾病，其特征为上呼吸道或胃肠道黏膜反复出现水肿。本病例报告的目的是提高急诊医生对一种可发展为获得性C1酯酶抑制剂缺乏所致血管性水肿的类腹膜炎病症的认识，从而有助于防止导致不必要手术干预的误诊。我们报告一例21岁男性患者，其因腹痛就诊于急诊科。他后来被诊断为获得性C1酯酶缺乏所致胃肠道血管性水肿，最初被怀疑为腹膜炎。在急诊科，对获得性C1酯酶缺乏患者的急腹症进行仔细评估对于区分急腹症的内科和外科病因非常重要。
