Tomà P, Lucigrai G, Pelizza A
Department of Radiology, Giannina Gaslini Children Institute, Genoa, Italy.
J Clin Ultrasound. 1991 Mar-Apr;19(3):155-61. doi: 10.1002/jcu.1870190306.
We have reviewed 5 cases of Caroli's disease, studied from 1982 to 1987, in order to define the validity of its sonographic signs. The "intraluminal portal vein" sign, found in all the cases, is emphasized. This sign may be easily identified and it is never encountered in other diseases. Recessive polycystic kidney disease was present in 3 cases, and congenital hepatic fibrosis was demonstrated in the 2 cases studied by liver biopsy.
我们回顾了1982年至1987年研究的5例卡罗利病病例,以确定其超声征象的有效性。强调了在所有病例中均发现的“腔内门静脉”征象。该征象易于识别,且在其他疾病中从未出现。3例存在隐性多囊肾病,通过肝活检研究的2例显示有先天性肝纤维化。