Guntupalli Saketh, Anderson Matthew Linley, Bodurka Diane C
Division of Gynecologic Oncology, Department of Obstetrics and Gynecology, Baylor College of Medicine, 1709 Dryden Road, Houston, TX 77030, USA.
Arch Gynecol Obstet. 2009 Feb;279(2):263-5. doi: 10.1007/s00404-008-0700-x. Epub 2008 Jun 12.
Alveolar soft part sarcoma (ASPS) is a rare mesenchymal malignancy typically found in the extremities or chest of young adults. We present a case of an alveolar soft part sarcoma arising in the endocervix of a 38-year-old premenopausal woman. This cancer was treated by extrafascial hysterectomy. No evidence of metastatic disease was found after extensive surgical staging. Since treatment, she has since remained disease-free for more than 5 years without additional therapy. This is the second case of ASPS arising in the endocervix of which we are aware. Our observations suggest simple hysterectomy suffices for optimal clinical management of cervical ASPS and that surgical staging of this disease offers little prognostic benefit.
肺泡软组织肉瘤（ASPS）是一种罕见的间叶组织恶性肿瘤，通常发生于年轻成年人的四肢或胸部。我们报告一例发生于一名38岁绝经前女性宫颈内的肺泡软组织肉瘤病例。该癌症通过筋膜外子宫切除术进行治疗。广泛的手术分期后未发现转移疾病的证据。自治疗以来，她未经额外治疗已无病生存超过5年。这是我们所知的第二例发生于宫颈的ASPS病例。我们的观察结果表明，单纯子宫切除术足以对宫颈ASPS进行最佳临床管理，并且该疾病的手术分期对预后益处不大。
