Long Hong-Qing, Qin Qin, Xie Cong-Hua
Department of Cancer Radio-chemotherapy, Zhongnan Hospital and Cancer Center of Wuhan University, Donghu Road, Wuhan, Hubei, PR China.
J Med Case Rep. 2008 Jun 25;2:217. doi: 10.1186/1752-1947-2-217.
Pulmonary artery intimal sarcoma is a rare disease with no characteristic symptoms. It is difficult to diagnose early and is frequently misdiagnosed as a pulmonary embolism.
Here we report a case of pulmonary artery intimal sarcoma in a 54-year-old woman presenting with complaints of shortness of breath on exertion. Echocardiography and a computed tomography scan showed that the right pulmonary artery trunk was blocked by a low-density mass. The patient was diagnosed with pulmonary artery intimal sarcoma by pathology and a complete mass resection was performed. After experiencing 10 months of disease-free survival, she was re-admitted because of the recurrence and metastasis of the tumor. Radiotherapy and chemotherapy were performed; however, only limited success was achieved. The patient died 15 months after the initial onset of symptoms.
Some patients with intimal sarcoma of the pulmonary artery can benefit from radiotherapy and chemotherapy as well as surgery.
肺动脉内膜肉瘤是一种罕见疾病，无特征性症状。早期诊断困难，常被误诊为肺栓塞。
在此我们报告一例54岁女性肺动脉内膜肉瘤病例，患者主诉劳力性呼吸困难。超声心动图和计算机断层扫描显示右肺动脉主干被低密度肿块阻塞。经病理诊断为肺动脉内膜肉瘤，并进行了完整的肿块切除术。经历10个月无病生存期后，因肿瘤复发转移再次入院。进行了放疗和化疗，但仅取得有限成功。患者在症状首次出现15个月后死亡。
部分肺动脉内膜肉瘤患者可从放疗、化疗以及手术中获益。
