Djordjevic Ivanka, Pejcic Tatjana, Rancic Milan, Radovic Milan, Bosnjakovic Petar, Radjenovic-Petkovic Tatjana, Nastasijevic-Borovac Desa, Golubovic Slavica, Dacic Dragana
The Clinical Center Nis, Clinic for lung diseases, Department for non specific lung diseases, Bul, Dr, Zorana Djindjica 48, 18 000 Nis, Republic of Serbia .
J Med Case Rep. 2009 Feb 16;3:64. doi: 10.1186/1752-1947-3-64.
Pulmonary artery sarcomas are rare neoplasms that are often confused with chronic thrombo-embolic disease, as both can have similar clinical and imaging presentation.
In this report, we present a case of a 50-year-old man initially diagnosed with chronic thrombo-embolic pulmonary disease, but who was later found to have pulmonary artery sarcoma with poor survival prognosis. We review the clinical and imaging characteristics of the two diseases and discuss the difficulties in establishing a timely diagnosis.
Similar clinical features and imaging presentation of pulmonary artery sarcoma and chronic thrombo-embolic pulmonary disease make definitive diagnosis difficult. This case report also illustrates and emphasizes that in any case with no predisposition factors for embolism, no evidence of deep venous thrombosis and pulmonary emboli, and inadequate relief of symptoms with anticoagulation, an alternative diagnosis of pulmonary artery sarcoma should be considered. If pulmonary artery sarcoma is diagnosed late in the course of the disease, there is usually a poor survival outcome.
肺动脉肉瘤是一种罕见的肿瘤，常与慢性血栓栓塞性疾病相混淆，因为两者可能具有相似的临床和影像学表现。
在本报告中，我们介绍了一例50岁男性患者，最初被诊断为慢性血栓栓塞性肺疾病，但后来被发现患有肺动脉肉瘤，生存预后较差。我们回顾了这两种疾病的临床和影像学特征，并讨论了及时确诊的困难。
肺动脉肉瘤和慢性血栓栓塞性肺疾病相似的临床特征和影像学表现使得明确诊断困难。本病例报告还说明并强调，在任何没有栓塞易患因素、没有深静脉血栓形成和肺栓塞证据且抗凝治疗后症状缓解不充分的病例中，应考虑肺动脉肉瘤的替代诊断。如果在疾病过程中肺动脉肉瘤诊断较晚，通常生存结果较差。
