Lee P, Bush A, Warner J O
Department of Paediatric, National Heart and Lung Institute, London.
Thorax. 1991 Jun;46(6):459-61. doi: 10.1136/thx.46.6.459.
The cause of the Williams Campbell syndrome (bronchomalacia with bronchiectasis) is controversial. A boy with bronchomalacia, bifid ribs, and left bronchial isomerism presented with intractable wheeze mimicking asthma. The combination of the abdominal, bronchial, and atrial anatomy seen in this child has been described only once previously. The coexistence of these congenital abnormalities in this boy supports a congenital cause for the Williams Campbell syndrome. The need to assess wheezy children critically is emphasised.
威廉姆斯·坎贝尔综合征（伴有支气管扩张的支气管软化症）的病因存在争议。一名患有支气管软化症、肋骨分叉和左支气管异构的男孩出现了类似哮喘的顽固性喘息。此前仅见过一次该患儿腹部、支气管和心房解剖结构的这种组合。这个男孩中这些先天性异常的共存支持了威廉姆斯·坎贝尔综合征的先天性病因。强调了对喘息儿童进行严格评估的必要性。
