Gastineau D A, Gertz M A, Rosen C B, Kyle R A
Division of Hematology and Internal Medicine, Mayo Clinic, Rochester, Minnesota.
Am J Hematol. 1991 Jul;37(3):194-6. doi: 10.1002/ajh.2830370312.
Hepatic rupture in primary systemic amyloidosis is extremely ominous; death occurs in hours to days. We present two cases of hepatic rupture diagnosed ante mortem with computed tomography (CT). Surgical repair was possible in one instance and successfully controlled the bleeding. In the setting of primary amyloidosis, the early use of CT scanning for undiagnosed ascites, hypotension, or rapid organ enlargement may lead to early diagnosis and potential surgical correction.
原发性系统性淀粉样变性中的肝破裂极其凶险,数小时至数天内即可导致死亡。我们报告两例经计算机断层扫描(CT)生前诊断为肝破裂的病例。其中一例可行手术修复,成功控制了出血。在原发性淀粉样变性的情况下,对于未确诊的腹水、低血压或器官迅速肿大早期使用CT扫描可能会实现早期诊断及潜在的手术矫正。