Jatene Marcelo Biscegli, Jatene Ieda Biscegli, Oliveira Patrícia Marques de, Moysés Rafael Aon, Souza Luis Carlos Bento de, Fontes Valmir, Miura Nana, Lopes Antonio Augusto, Marcial Miguel Barbero, Jatene Adib Domingos
Instituto do Coração, Hospital das Clínicas, Faculdade de Medicina, Universidade de São Paulo.
Arq Bras Cardiol. 2008 Jul;91(1):17-24. doi: 10.1590/s0066-782x2008001300003.
The Transposition of the Great Arteries is the most frequent congenital cyanogenic cardiopathy in the neonatal period, corresponding to 7% of all congenital cardiopathies. Among the operations for surgical treatment, the Jatene operation, with arterial correction, is the treatment of choice. During the late postoperative evolution, some problems were observed, with the most common being the occurrence of supravalvular stenosis at the neopulmonary, regardless of the type of surgical technique used.
To study and analyze the prevalence of stenosis, as well as describe the surgical treatment and propose technical maneuvers to prevent its onset.
Of the 553 patients that underwent surgery, 409 were discharged from the hospital and 281 had late follow-up; 59 (20.9%) presented different degrees of supravalvular pulmonary stenosis and 21 had a mean gradient > 60 mmHg, needing surgical treatment. Depending on the location and anatomy of the stenosis, the surgical treatment consisted of the use of different techniques, such as the enlargement of stenosis areas with bovine pericardium patches, resection of stenotic areas and termino-terminal anastomosis, replacement of retracted patches and synthetic tubes.
Twenty patients presented good evolution and only one patient died.
It can be concluded that the supravalvular pulmonary stenosis, post-Jatene operation for Transposition of Great Arteries, had a prevalence of 20.9%; once identified and with indication for treatment, it can be treated surgically with low mortality levels, through different surgical techniques; to prevent the occurrence of stenosis, ample dissection and release of the pulmonary branches, double anastomoses, large patches of autologous pericardium and careful reconstruction of the aorta are proposed, which prevents the compression of the neopulmonary.
大动脉转位是新生儿期最常见的先天性青紫型心脏病,占所有先天性心脏病的7%。在手术治疗方法中,采用动脉矫正的贾腾手术是首选治疗方法。在术后晚期演变过程中,观察到一些问题,最常见的是新肺动脉瓣上狭窄的发生,无论采用何种手术技术。
研究和分析狭窄的发生率,描述手术治疗方法,并提出预防其发生的技术操作。
在接受手术的553例患者中,409例出院,281例进行了晚期随访;59例(20.9%)出现不同程度的肺动脉瓣上狭窄,21例平均压差>60 mmHg,需要手术治疗。根据狭窄的部位和解剖结构,手术治疗包括采用不同的技术,如用牛心包补片扩大狭窄区域、切除狭窄区域并进行端端吻合、更换回缩的补片和合成管道。
20例患者病情好转,仅1例死亡。
可以得出结论,大动脉转位贾腾手术后肺动脉瓣上狭窄的发生率为20.9%;一旦确诊并有治疗指征,可通过不同的手术技术进行手术治疗,死亡率较低;为预防狭窄的发生,建议充分解剖和松解肺分支、进行双重吻合、使用大的自体心包补片并仔细重建主动脉,以防止新肺动脉受压。