Gut. 1974 May;15(5):396-400. doi: 10.1136/gut.15.5.396.
Of 27 patients with liver disease and cryoglobulinaemia 18 proved to have paraproteins. Six of these monoclonal immunoglobulins were shown to have antibody activity, directed to human gamma globulin, alpha(1)-fetoprotein, smooth muscle, and mitochondria.Eight of the patients suffered from acute viral hepatitis, five of whom were HB Ag positive; in all these cases the monoclonal spikes were transient and their antibody activities were directed against IgG in two cases and alpha(1)-fetoprotein in one.Seven of the patients had active chronic hepatitis and in these the paraproteinaemia persisted, though remaining quantitatively unchanged over several years. One of them had a cryoprecipitable monoclonal smooth muscle antibody. Three patients had primary biliary cirrhosis and in two of them monoclonal IgM mitochondrial antibodies were demonstrated.In three out of the 18 cases there was a double M-component.Since these monoclonal antibodies are directed to autoantigens not unlike the polyclonal ones usually seen in autoimmune hepatic diseases, it is suggested that the factor which triggers the uncontrolled plasma cell proliferation to produce paraproteins must meet cells from an already expanding clone.
在 27 例肝脏疾病伴冷球蛋白血症的患者中,18 例证实存在单克隆蛋白。这些单克隆免疫球蛋白中,有 6 种表现出抗体活性,针对人 γ 球蛋白、α1-胎蛋白、平滑肌和线粒体。8 例患者患有急性病毒性肝炎,其中 5 例乙型肝炎表面抗原阳性;在所有这些情况下,单克隆峰是短暂的,其抗体活性在两种情况下针对 IgG,在一种情况下针对 α1-胎蛋白。7 例患者患有活动性慢性肝炎,这些患者的冷球蛋白血症持续存在,尽管在几年内数量保持不变。其中 1 例有可沉淀的单克隆平滑肌抗体。3 例患者患有原发性胆汁性肝硬化,其中 2 例患者证实存在单克隆 IgM 线粒体抗体。在 18 例中有 3 例存在双 M 成分。由于这些单克隆抗体针对的是不同于自身免疫性肝疾病中常见的多克隆自身抗原,因此,触发不受控制的浆细胞增殖产生单克隆蛋白的因素必须与已经扩增的克隆的细胞相遇。