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扩张型心肌病患者切除嗜铬细胞瘤后左心室射血分数恢复正常。

Normalization of left ventricular ejection fraction following resection of pheochromocytoma in a patient with dilated cardiomyopathy.

作者信息

Hicks R J, Wood B, Kalff V, Anderson S T, Kelly M J

机构信息

Department of Nuclear Medicine, Alfred Hospital, Melbourne, Australia.

出版信息

Clin Nucl Med. 1991 Jun;16(6):413-6. doi: 10.1097/00003072-199106000-00007.

DOI:10.1097/00003072-199106000-00007
PMID:1868653
Abstract

Catecholamine-induced cardiomyopathy associated with pheochromocytoma is a well-recognized but rare entity. Both hypertrophic and dilated variants have been described. We report a case of dilated cardiomyopathy associated with a benign pheochromocytoma that showed complete normalization of left ventricular systolic function following removal of the tumor. Serum noradrenaline and dopamine were significantly elevated without elevation in serum adrenaline levels. This may be the first report in which radionuclide ventriculography was used to document the time course of normalization in LVEF following removal of a pheochromocytoma.

摘要

儿茶酚胺诱导的心肌病与嗜铬细胞瘤相关,是一种已被充分认识但罕见的病症。肥厚型和扩张型变体均有描述。我们报告一例与良性嗜铬细胞瘤相关的扩张型心肌病病例,该病例在肿瘤切除后左心室收缩功能完全恢复正常。血清去甲肾上腺素和多巴胺显著升高,而血清肾上腺素水平未升高。这可能是首例使用放射性核素心室造影记录嗜铬细胞瘤切除后左心室射血分数(LVEF)恢复正常时间进程的报告。

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Normalization of left ventricular ejection fraction following resection of pheochromocytoma in a patient with dilated cardiomyopathy.扩张型心肌病患者切除嗜铬细胞瘤后左心室射血分数恢复正常。
Clin Nucl Med. 1991 Jun;16(6):413-6. doi: 10.1097/00003072-199106000-00007.
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引用本文的文献

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Pheochromocytoma-Induced Reversible Dilated Cardiomyopathy: A Case Report and Literature Review.嗜铬细胞瘤所致可逆性扩张型心肌病:一例报告及文献复习
Clin Case Rep. 2025 Mar 7;13(3):e70241. doi: 10.1002/ccr3.70241. eCollection 2025 Mar.
2
An unusual case of cardiomyopathy in a 75-year-old woman.一名75岁女性患心肌病的罕见病例。
Neth Heart J. 2005 Feb;13(2):62-64.
3
Severe reversible dilated cardiomyopathy in a patient with multiple endocrine neoplasia 2A syndrome.一名患有多发性内分泌腺瘤病2A型综合征的患者出现严重可逆性扩张型心肌病。
J Endocrinol Invest. 2006 Apr;29(4):363-6. doi: 10.1007/BF03344110.
4
Pheochromocytoma as an endocrine emergency.嗜铬细胞瘤作为一种内分泌急症。
Rev Endocr Metab Disord. 2003 May;4(2):121-8. doi: 10.1023/a:1022981801344.
5
[The use of magnesium sulfate during surgery of pheochromocytoma: apropos of 2 cases].[嗜铬细胞瘤手术中硫酸镁的应用:附2例报告]
Can J Anaesth. 1993 Jun;40(6):521-5. doi: 10.1007/BF03009735.