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[肾肿大:婴儿急性淋巴细胞白血病的一种不寻常表现]

[Nephromegaly: as unusual presentation of acute lymphoblastic leukemia in an infant].

作者信息

Martins Andrea, Cairoli Héctor, Domínguez Paula, Martin Sandra, Ortiz Corina, Potasznik Javier, Schenone Norma

机构信息

Hospital de Niños Dr. Pedro de Elizalde.

出版信息

Arch Argent Pediatr. 2008 Jun;106(3):263-5. doi: 10.1590/S0325-00752008000300013.

DOI:10.1590/S0325-00752008000300013
PMID:18695841
Abstract

Nephromegaly in infancy may be due to several causes, being the most relevant: renal polycystic autosomic recessive disease, venous renal thrombosis, deposit diseases, kidney tumors, nephrotic congenital syndrome and neoplastic infiltration. Although renal infiltration is relatively frequent in acute lymphoblastic leukemia, nephromegaly is an unusual form of presentation in this pathology. The case of a four-year-old patient, who presents bilateral nephromegaly and pancytopenia, is presented. Acute Lymphoblastic Leukemia is diagnosed, initiating the corresponding chemotherapic treatment.

摘要

婴儿期肾肿大可能由多种原因引起,其中最相关的有:常染色体隐性遗传性多囊肾病、肾静脉血栓形成、沉积性疾病、肾肿瘤、先天性肾病综合征和肿瘤浸润。虽然肾浸润在急性淋巴细胞白血病中相对常见,但肾肿大在这种病理情况下是一种不常见的表现形式。本文介绍了一名4岁患者的病例,该患者出现双侧肾肿大和全血细胞减少。诊断为急性淋巴细胞白血病,并开始相应的化疗。

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1
[Nephromegaly: as unusual presentation of acute lymphoblastic leukemia in an infant].[肾肿大:婴儿急性淋巴细胞白血病的一种不寻常表现]
Arch Argent Pediatr. 2008 Jun;106(3):263-5. doi: 10.1590/S0325-00752008000300013.
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Precursor B-cell acute lymphoblastic leukemia: An unusual cause of bilateral nephromegaly in an infant.前体B细胞急性淋巴细胞白血病:婴儿双侧肾肿大的罕见病因。
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Massive bilateral nephromegaly in acute lymphoblastic leukemia: a case report.急性淋巴细胞白血病中的双侧巨大肾肿大:一例报告
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Renal biopsy diagnosis of acute lymphocytic leukemia.急性淋巴细胞白血病的肾活检诊断
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Acute lymphoblastic leukemia presenting as bilateral renal enlargement in a child.一名儿童急性淋巴细胞白血病表现为双侧肾脏肿大。
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Bilateral parotid gland enlargement and palpable nephromegaly in infant acute lymphoblastic leukemia: case report and review of the literature.婴儿急性淋巴细胞白血病中的双侧腮腺肿大及可触及的肾肿大:病例报告及文献复习
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Bilateral nephromegaly simulating wilms tumor: a rare initial manifestation of acute lymphoblastic leukemia.双侧肾肿大酷似肾母细胞瘤:急性淋巴细胞白血病罕见的初始表现。
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引用本文的文献

1
Extramedullary manifestations in acute lymphoblastic leukemia in children: a systematic review and guideline-based approach of treatment.儿童急性淋巴细胞白血病的髓外表现:一项基于系统评价和指南的治疗方法
Am J Blood Res. 2020 Dec 15;10(6):360-374. eCollection 2020.
2
Renal involvement at diagnosis of pediatric acute lymphoblastic leukemia.小儿急性淋巴细胞白血病诊断时的肾脏受累情况。
Pediatr Rep. 2020 Apr 8;12(1):8382. doi: 10.4081/pr.2020.8382. eCollection 2020 Feb 11.
3
Precursor B-cell acute lymphoblastic leukemia: An unusual cause of bilateral nephromegaly in an infant.
前体B细胞急性淋巴细胞白血病:婴儿双侧肾肿大的罕见病因。
J Postgrad Med. 2017 Oct-Dec;63(4):271-272. doi: 10.4103/jpgm.JPGM_231_17.
4
Acute lymphoblastic leukemia: an unusual cause of nephromegaly in infancy.急性淋巴细胞白血病:婴儿期肾肿大的一种罕见病因。
Indian J Pediatr. 2010 May;77(5):583. doi: 10.1007/s12098-010-0028-y.