Dryzek Paweł, Mazurek-Kula Anna, Moszura Tomasz, Sysa Andrzej
Department of Cardiology, Polish Mother's Memorial Hospital, Research Institute, Łódź, Poland.
Cardiol J. 2008;15(4):376-9.
We present the case of a 3-month-old infant with tetralogy of Fallot (ToF) with pulmonary artery hypoplasia, critical right ventricle outflow tract (RVOT) obstruction and the presence of major aortopulmonary collateral arteries (MAPCA) and CATCH 22 syndrome. Due to anatomical conditions (severe pulmonary artery hypoplasia), the patient was not qualified for palliative operative treatment Blalock-Taussig shunt. We conducted catheterization with an attempt of balloon plasty and stent implantation into the right ventricle outflow tract and main pulmonary artery. Successful stent implantation into the right ventricle outflow tract was performed. The stent created a 4.1 mm diameter channel and allowed for unrestricted blood flow from the right ventricle to the pulmonary arteries. After the procedure we observed an increase in blood saturation of up to 89%. Control echocardiography revealed blood flow through the stent to the pulmonary arteries with a pressure gradient of 45 mm Hg. There were neither rhythm nor conduction disturbances in the control ECG after the procedure. After 6 days of observation the patient was discharged from our department. We conclude that successful stent implantation into the RVOT in patients with ToF and hypoplastic pulmonary arteries improves their clinical condition, increases pulmonary blood flow by physiological means and leads to an improvement of pulmonary artery development before surgical treatment.
我们报告了一例3个月大的患有法洛四联症(ToF)的婴儿病例,该患儿伴有肺动脉发育不全、严重的右心室流出道(RVOT)梗阻、存在主-肺动脉侧支动脉(MAPCA)以及22q11.2微缺失综合征(CATCH 22综合征)。由于解剖学条件(严重的肺动脉发育不全),该患者不符合姑息性手术治疗(Blalock-Taussig分流术)的条件。我们进行了导管插入术,尝试对右心室流出道和主肺动脉进行球囊成形术和支架植入。成功地在右心室流出道植入了支架。该支架形成了一个直径为4.1毫米的通道,使血液能够从右心室无阻碍地流向肺动脉。术后我们观察到血液饱和度提高到了89%。对照超声心动图显示有血液通过支架流向肺动脉,压力梯度为45毫米汞柱。术后对照心电图未发现节律或传导紊乱。经过6天的观察,患者从我们科室出院。我们得出结论,对于患有ToF和发育不全肺动脉的患者,成功地在RVOT植入支架可改善其临床状况,通过生理手段增加肺血流量,并在手术治疗前促进肺动脉发育。