Benmously-Mlika R, Deghais S, Bchetnia M, Charfeddine C, Mokni M, Kassar S, Haouet S, Boubaker S, Mokhtar I, Abdelhak S, Dhahri A Ben Osman
Dermatology Department, Habib Thameur Hospital, Tunis, Tunisia.
Dermatol Online J. 2008 Jun 15;14(6):15.
Supernumerary nipples (SNs) or polythelia are developmental abnormalities of breast tissue. They are located along the embryonic mammary lines. Polythelia usually occurs as a sporadic abnormality, although familial aggregation has been occasionally reported. Hailey-Hailey disease is a rare autosomal genodermatosis characterized by disturbed keratinocyte adhesion. These cutaneous disorders have been described in correlation with many other abnormalities. We report here the association of Hailey-Hailey disease and supernumerary nipples in a Northern Tunisian family. To our knowledge, this is the first report of such a clinical association.
副乳头（SNs）或多乳头症是乳腺组织的发育异常。它们沿着胚胎乳腺线分布。多乳头症通常表现为散发性异常，尽管偶尔有家族聚集的报道。黑利-黑利病是一种罕见的常染色体遗传性皮肤病，其特征是角质形成细胞黏附障碍。这些皮肤疾病已被描述与许多其他异常有关。我们在此报告突尼斯北部一个家族中黑利-黑利病与副乳头的关联。据我们所知，这是这种临床关联的首次报告。
