Smith Pearl M, Abdalla W M A, Lin D D M, Comi A M, Boltshauser E, Gailloud P, Huisman T A G M
Johns Hopkins Hospital, Baltimore, MD, USA.
J Neuroradiol. 2009 Mar;36(1):57-60. doi: 10.1016/j.neurad.2008.07.008. Epub 2008 Aug 21.
Sturge-Weber syndrome is a rare neurocutaneous disorder that typically presents with angiomas involving the face, ocular choroid and ipsilateral supratentorial leptomeninges. Posterior fossa involvement is extremely rare. We present two patients with simultaneous supra- and infratentorial involvement. Magnetic resonance imaging (MRI) and digital subtracted angiography (DSA) findings are discussed.
斯特奇-韦伯综合征是一种罕见的神经皮肤疾病,通常表现为累及面部、眼脉络膜和同侧幕上软脑膜的血管瘤。后颅窝受累极为罕见。我们报告了两名同时有幕上和幕下受累的患者。讨论了磁共振成像(MRI)和数字减影血管造影(DSA)的结果。