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皮下脂膜炎样T细胞淋巴瘤及其他主要累及皮下组织的原发性皮肤淋巴瘤。

Subcutaneous panniculitic-like T-cell lymphoma and other primary cutaneous lymphomas with prominent subcutaneous tissue involvement.

作者信息

Gallardo Fernando, Pujol Ramon M

机构信息

Department of Dermatology, Hospital del Mar. IMAS, Passeig Marítim 25-29, 08003 Barcelona, Spain.

出版信息

Dermatol Clin. 2008 Oct;26(4):529-40, viii. doi: 10.1016/j.det.2008.05.008.

DOI:10.1016/j.det.2008.05.008
PMID:18793987
Abstract

The concept of subcutaneous T-cell lymphoma defines a reduced group of primary cutaneous lymphomas characterized morphologically by a prominent or exclusive subcutaneous tissue involvement. Subcutaneous panniculitic-like T-cell lymphoma is a rare subtype of primary cutaneous T-cell lymphoma clinically mimicking panniculitis. The clinical course is usually protracted with recurrent cutaneous lesions but rarely with early extracutaneous dissemination. The clinical, histopathologic, immunophenotypic, and evolutive features of this heterogeneous and rare group of primary cutaneous lymphomas are reviewed.

摘要

皮下T细胞淋巴瘤的概念定义了一组原发性皮肤淋巴瘤,其形态学特征为显著或仅累及皮下组织。皮下脂膜炎样T细胞淋巴瘤是原发性皮肤T细胞淋巴瘤的一种罕见亚型,临床上酷似脂膜炎。临床病程通常迁延,有复发性皮肤损害,但很少早期出现皮肤外播散。本文对这一异质性罕见原发性皮肤淋巴瘤组的临床、组织病理学、免疫表型及演变特征进行综述。

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