Lester Laura, Ewalt Mark, Warnke Roger, Kim Jinah
Department of Pathology, Stanford University Medical School, Stanford, CA, USA.
J Cutan Pathol. 2015 Jan;42(1):46-9. doi: 10.1111/cup.12436. Epub 2014 Dec 9.
Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is an uncommon non-Hodgkins primary cutaneous lymphoma that typically presents as subcutaneous nodules on the extremities or trunk. Here, we report an unusual case of systemic panniculitic T-cell lymphoma with predominantly mesenteric extra-cutaneous involvement and an aggressive clinical course with histopathologic and immunophenotypic features that mimic SPTCL. This case serves to expand the body of literature regarding systemic SPTCL-like disorders with prominent extra-cutaneous involvement.
皮下脂膜炎样T细胞淋巴瘤(SPTCL)是一种罕见的非霍奇金原发性皮肤淋巴瘤,通常表现为四肢或躯干的皮下结节。在此,我们报告一例不寻常的系统性脂膜炎性T细胞淋巴瘤病例,主要累及肠系膜等皮肤外部位,临床病程侵袭,组织病理学和免疫表型特征类似SPTCL。该病例有助于扩充关于具有显著皮肤外累及的系统性SPTCL样疾病的文献。