Wang Dee Dee, Kasapis Christos, Nallamothu Brahmajee K
University of Michigan Health System, Ann Arbor, MI 48109-5368, USA.
J Invasive Cardiol. 2008 Oct;20(10):E296-300.
Spontaneous hemopericardium is extremely rare in patients with hemophilia and has never been reported in hemophilia B-factor IX deficiency. We report a patient with hemophilia B who presented with spontaneous hemopericardium and tamponade requiring emergent pericardiocentesis. As advances in therapies improve the longevity and quality of life of patients with hemophilia, it is likely that adult interventional cardiologists will increasingly encounter these patients in the cardiac catheterization laboratory. We review the clinical challenges raised by this group of patients undergoing cardiac procedures and present a stepwise approach to optimal management during the periprocedural period.
自发性心包积血在血友病患者中极为罕见，而在B型血友病（因子IX缺乏症）患者中从未有过报道。我们报告了一名B型血友病患者，该患者出现自发性心包积血并伴有心脏压塞，需要紧急进行心包穿刺术。随着治疗方法的进步提高了血友病患者的寿命和生活质量，成年介入心脏病专家在心脏导管实验室中越来越有可能遇到这些患者。我们回顾了这组接受心脏手术的患者所带来的临床挑战，并提出了围手术期优化管理的逐步方法。
