Sakai Mio, Aoki Shigeki, Inoue Yusuke, Ashida Ryuichi, Yamada Haruyasu, Kiryu Shigeru, Inano Sachiko, Mori Harushi, Masutani Yoshitaka, Abe Osamu, Ohtomo Kuni, Nakamura Hironobu
Department of Radiology, The Institute of Medical Science, University of Tokyo, Tokyo, Japan.
J Comput Assist Tomogr. 2008 Sep-Oct;32(5):822-4. doi: 10.1097/RCT.0b013e318153fd60.
We report a patient with linear scleroderma en coup de sabre without neurological symptoms despite the presence of large white matter lesions. The patient underwent 3.0-T magnetic resonance (MR) examinations including diffusion tensor imaging, time-resolved contrast-enhanced MR angiography, susceptibility-weighted imaging, and proton MR spectroscopy. These imaging findings suggested increased vascular permeability and microbleeding without abnormalities of metabolites. Our observation is consistent with vasculopathy and may be helpful in the proper diagnosis and treatment of linear scleroderma en coup de sabre.
我们报告了一名患有剑伤样线状硬皮病的患者，尽管存在大量白质病变，但无神经症状。该患者接受了3.0-T磁共振（MR）检查，包括扩散张量成像、时间分辨对比增强MR血管造影、磁敏感加权成像和质子MR波谱分析。这些影像学表现提示血管通透性增加和微出血，代谢物无异常。我们的观察结果与血管病变一致，可能有助于剑伤样线状硬皮病的正确诊断和治疗。
