Gao Zeng-Xin, Weng Xi-Sheng, Qiu Gui-Xing, Zhao Yong-Qiang, Shao Bai, Lin Jin, Wang Xue-Song, Yang Xin-Yu
Department of Orthopedic Surgery, Peking Union Medical College Hospital, Chinese Academy of Medical Science and Peking Union Medical College, Beijing 100730, China.
Zhonghua Yi Xue Za Zhi. 2008 Apr 29;88(17):1181-4.
To analyze the clinical manifestations and imaging features of hemophilic pseudotumor.
Eight patients with hemophilic pseudotumor, all males, aged 26.1 (18 -38), were hospitalized, underwent resection of pseudotumor and bone reconstruction, and followed up for 38.6 months (7 months to 11 years). The clinical data were analyzed.
Femur was involved in 4 patient, and fifth metacarpus, iliopsoas, quadriceps femoris, and gastrocnemius were involved in 1 patient respectively. No recurrence was found. Excellent healing was seen in 6 cases, claudication occurred in 1 case with shortening femur, while unpleasant outcome happened to 1 case because of formation of clotting factor inhibitor, together with poor wound-healing waiting for amputation.
Medical history and imaging features are essential for the diagnosis of hemophilic pseudotumor. It is the key for successful treatment to master its clinical characteristics.
分析血友病性假肿瘤的临床表现及影像学特征。
8例血友病性假肿瘤患者均为男性，年龄26.1岁（18 - 38岁），住院后行假肿瘤切除及骨重建，并随访38.6个月（7个月至11年）。对临床资料进行分析。
4例累及股骨，1例分别累及第五掌骨、髂腰肌、股四头肌和腓肠肌。无复发。6例愈合良好，1例因股骨缩短出现跛行，1例因形成凝血因子抑制剂且伤口愈合不良等待截肢，预后不佳。
病史及影像学特征对血友病性假肿瘤的诊断至关重要。掌握其临床特点是治疗成功的关键。
