von der Oelsnitz G, Spaar H J, Lieber T, Münchow B, Booss D
Kinderchirurgische Klinik des Zentralkrankenhauses St. Jürgen-Strasse Bremen.
Eur J Pediatr Surg. 1991 Jun;1(3):161-5. doi: 10.1055/s-2008-1042479.
A 2 4/12-year-old boy with obstructive jaundice caused by a tumor of the portal area that proved to be an embryonal rhabdomyosarcoma of the common bile duct is reported. The diagnosis was made clinically, radiographically, ultrasonographically, and histologically. Surgery was elected as the primary therapy; there were no intra- or postoperative complications. The prognosis and its improvement by means of aggressive chemotherapy and local irradiation are discussed.
报告了一名2又4/12岁的男孩,其因门静脉区肿瘤导致梗阻性黄疸,该肿瘤经证实为胆总管胚胎性横纹肌肉瘤。诊断通过临床、放射学、超声检查及组织学方法做出。手术被选为主要治疗方法;术中及术后均无并发症。文中讨论了预后情况以及通过积极化疗和局部放疗改善预后的方法。