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[慢性炎症性脱髓鞘性多发性神经根神经病的诊断策略。法国工作组的建议]

[Diagnostic strategy for chronic inflammatory demyelinating polyradiculoneuropathy. Recommendations of the French working group].

作者信息

Magy L

机构信息

Service de neurologie, centre de référence des neuropathies périphériques rares, CHRU Dupuytren, 2, avenue Martin-Luther-King, 87042 Limoges cedex, France.

出版信息

Rev Neurol (Paris). 2008 Dec;164(12):1063-7. doi: 10.1016/j.neurol.2008.09.001. Epub 2008 Oct 23.

DOI:10.1016/j.neurol.2008.09.001
PMID:18950823
Abstract

The diagnosis of chronic inflammatory demyelinating polyradiculoneuropathy (CIDP) requires a careful clinical and neurophysiological evaluation, often completed by CSF analysis. In numerous cases, this diagnosis is straightforward and leads to rapid initiation of an immunomodulatory treatment. However, some patients are not diagnosed because of atypical clinical and/or neurophysiological features, and do not benefit from a potentially effective treatment. In this context, a working group was composed with the task of establishing recommendations on diagnostic strategies for CIDP in the main clinical situations where this diagnosis may be suspected. We have summarized these recommendations and tried to present them in the form of a decision-making algorithm.

摘要

慢性炎症性脱髓鞘性多发性神经根神经病(CIDP)的诊断需要仔细的临床和神经生理学评估,通常还需进行脑脊液分析来完成。在许多病例中,这种诊断很直接,能迅速启动免疫调节治疗。然而,一些患者因临床和/或神经生理学特征不典型而未被诊断,无法从可能有效的治疗中获益。在此背景下,成立了一个工作组,其任务是针对可能怀疑CIDP诊断的主要临床情况制定诊断策略建议。我们总结了这些建议,并试图以决策算法的形式呈现。

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