磷酸戊糖途径的生物化学、代谢及遗传缺陷：综述
The biochemistry, metabolism and inherited defects of the pentose phosphate pathway: a review.
作者信息
Wamelink M M C, Struys E A, Jakobs C
机构信息
Metabolic Unit, Department of Clinical Chemistry, VU University Medical Center, De Boelelaan 1117, 1081 HV, Amsterdam, The Netherlands.
出版信息
J Inherit Metab Dis. 2008 Dec;31(6):703-17. doi: 10.1007/s10545-008-1015-6. Epub 2008 Nov 8.
The recent discovery of two defects (ribose-5-phosphate isomerase deficiency and transaldolase deficiency) in the reversible part of the pentose phosphate pathway (PPP) has stimulated interest in this pathway. In this review we describe the functions of the PPP, its relation to other pathways of carbohydrate metabolism and an overview of the metabolic defects in the reversible part of the PPP.
最近在磷酸戊糖途径（PPP）的可逆部分发现了两种缺陷（核糖-5-磷酸异构酶缺乏症和转醛醇酶缺乏症），这引发了人们对该途径的兴趣。在这篇综述中，我们描述了PPP的功能、它与碳水化合物代谢其他途径的关系，以及对PPP可逆部分代谢缺陷的概述。
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