Putz C, Stierle I, Grieser T, Mohr G, Gerner H J, Fürstenberg C H, Wiedenhöfer B
Department of Spine Surgery and Spinal Cord Injury Center, Orthopaedic University Hospital Heidelberg, Heidelberg, Germany.
Spinal Cord. 2009 Jul;47(7):570-2. doi: 10.1038/sc.2008.133. Epub 2008 Nov 11.
Case report.
To describe a rare case of paraplegia in a patient with Scheuermann's disease and dysplastic thoracic spinous processes.
Spinal Cord Injury Center, Orthopaedic University Hospital Heidelberg, Heidelberg, Germany.
The authors report on a 15-year-old boy with progressive incomplete spastic paraplegia presenting segmental dysplastic thoracic spinous processes and Scheuermann's disease. The magnetic resonance imaging showed a kyphotic angulation at T 5/6 and signs of myelopathy. Hypoplastic thoracic processes and hypoplastic paraspinal muscles in the upper thoracic spine were observed intraoperatively. In this case, dorsoventral stabilization from T 4-7 was performed and the neurological outcome improved at follow-up (6 months).
Paraplegia can be accelerated in patients with Scheuermann's disease, severe kyphotic angulation and dysplastic posterior elements. After operative treatment, neurological recovery and a normal walking pattern were shown.
病例报告。
描述一例患有休门氏病和发育异常的胸椎棘突的患者发生截瘫的罕见病例。
德国海德堡大学骨科医院脊髓损伤中心。
作者报告了一名15岁男孩，患有进行性不完全痉挛性截瘫，伴有节段性发育异常的胸椎棘突和休门氏病。磁共振成像显示T5/6处有后凸成角及脊髓病迹象。术中观察到胸椎上段棘突发育不全及椎旁肌发育不全。在此病例中，实施了T4 - 7节段的前后路稳定手术，随访（6个月）时神经功能结果有所改善。
患有休门氏病、严重后凸成角和发育异常的后部结构的患者，截瘫可能会加速发展。手术治疗后，显示出神经功能恢复和正常行走模式。
