原发性气管支气管淀粉样变性

Primary tracheobronchial amyloidosis.

作者信息

Santos José Wellington Alves dos, Schneider Filho Ayrton, Bertolazzi Alessandra, Michel Gustavo Trindade, Silva Lauro Vinícius Schvarcz da, Melo Carlos Renato, Pedro Vinícius Dallagasperina, Spilmann Daniel, Figaro Juliana Kaczmareck

机构信息

Departmento de Residência Médica, Ministério da Educação, Brasília, Brazil.

出版信息

J Bras Pneumol. 2008 Oct;34(10):881-4. doi: 10.1590/s1806-37132008001000015.

DOI:10.1590/s1806-37132008001000015

PMID:19009220

Abstract

Tracheobronchial amyloidosis is an uncommon localized form of amyloidosis, characterized by amyloid deposits restricted to the trachea, main bronchi and segmental bronchi. We present the case of a retired 67-year-old man with long-term progressive dyspnea, wheezing and chest pain. A diagnosis of tracheobronchial amyloidosis was made after the third fiberoptic bronchoscopy and histological confirmation through Congo red staining of tissue samples.

摘要

气管支气管淀粉样变是一种罕见的局限性淀粉样变，其特征是淀粉样沉积物局限于气管、主支气管和段支气管。我们报告一例67岁退休男性病例，该患者长期进行性呼吸困难、喘息和胸痛。在第三次纤维支气管镜检查及通过组织样本刚果红染色进行组织学确诊后，诊断为气管支气管淀粉样变。