Vieira Isabela Garcia, Marchiori Edson, Zanetti Gláucia, Cabral Rafael Ferracini, Takayassu Tatiana Chinem, Spilberg Gabriela, Batista Raquel Ribeiro
Service of Diagnostic Radiology, Clementino Fraga Filho Universitary Hospital, Rua Prof. Rodolpho Paulo Rocco, 225. CEP 21.941.913. Cidade Universitária. Rio de Janeiro, Brazil.
Cases J. 2009 Sep 8;2:6540. doi: 10.4076/1757-1626-2-6540.
Pulmonary amyloidosis is an uncommon disease, characterized by extracellular deposition of fibrillary protein in the lungs. It appears in three forms: tracheobronchial, nodular pulmonary, and alveolar septal. There are few reports of long-term observation of primary pulmonary amyloidosis.
We present the case of a 47-year-old man who presented with fever, dyspnea, cough and hemoptysis. Chest radiograph and computed tomography revealed multiple pulmonary nodules and masses. The patient underwent open lung biopsy, which diagnosed pulmonary amyloidosis.
Pulmonary nodular amyloidosis should be considered in the differential diagnosis of pulmonary nodules or masses.
肺淀粉样变性是一种罕见疾病,其特征为肺内纤维状蛋白的细胞外沉积。它以三种形式出现:气管支气管型、结节型肺淀粉样变性和肺泡间隔型。关于原发性肺淀粉样变性的长期观察报告很少。
我们报告一例47岁男性患者,其表现为发热、呼吸困难、咳嗽和咯血。胸部X线片和计算机断层扫描显示多个肺结节和肿块。患者接受了开胸肺活检,诊断为肺淀粉样变性。
在肺结节或肿块的鉴别诊断中应考虑肺结节型淀粉样变性。