Khosla Arjun, Ponsky Todd A
Division of Pediatric Surgery, Rainbow Babies and Children's Hospital, Case Western Reserve University, Cleveland, OH 44106, USA.
J Pediatr Surg. 2008 Dec;43(12):2281-4. doi: 10.1016/j.jpedsurg.2008.07.030.
Sickle cell disease is a disorder that produces significant morbidity and mortality. Vaso-occlusive pain crises are the most common presenting symptom associated with sickle cell patients. A rare, yet important to recognize, complication of sickle cell disease is acute colonic pseudoobstruction, also known as Ogilvie's syndrome. These patients may present with symptoms that are difficult to distinguish from other etiologies of abdominal pain, but a thorough diagnostic workup can provide important clues. Furthermore, there is no agreement on optimal treatment of pseudoobstruction. We report the first pediatric case of acute pseudoobstruction secondary to sickle cell disease that was treated successfully with neostigmine. Early recognition of this phenomenon is important as it alters patient management, can be treated medically, and may avoid unnecessary surgical intervention.
镰状细胞病是一种会导致严重发病和死亡的疾病。血管阻塞性疼痛危象是镰状细胞病患者最常见的症状。急性结肠假性梗阻,也称为奥吉尔维综合征,是镰状细胞病一种罕见但需要识别的重要并发症。这些患者的症状可能难以与其他腹痛病因相区分,但全面的诊断检查可以提供重要线索。此外,对于假性梗阻的最佳治疗方法尚无共识。我们报告了首例继发于镰状细胞病的急性假性梗阻儿科病例,该病例用新斯的明成功治疗。尽早识别这一现象很重要,因为它会改变患者的治疗管理,可以通过药物治疗,还可能避免不必要的手术干预。