Stokes K B
Children's Specialist Centre, Royal Children's Hospital Melbourne, Parkville, Victoria, Australia.
Prog Pediatr Surg. 1991;27:127-47. doi: 10.1007/978-3-642-87767-4_8.
Unusual varieties of diaphragmatic herniae can be classified into two major groups, congenital and acquired. The late-presenting Bochdalek herniae often present difficulties in diagnosis which may lead to inappropriate treatment. The prime example is the herniated stomach, which is mistaken for a tension pneumothorax. Strangulation is a rare, but an important, complication of Bochdalek herniae. A number of techniques for closure of large diaphragmatic defects are described with recommendation of those procedures which can be performed rapidly and effectively in a critically ill infant. The literature concerning eventration is confusing due to different definitions of the condition by different authors. It may be difficult to distinguish preoperatively between this condition and congenital diaphragmatic hernia with a sac. Such distinction is often not important as the decision for intervention is based on evaluation of clinical and radiological considerations. The majority of Morgagni herniae are asymptomatic and only rarely does strangulation supervene. There is a small group of infants with Morgagni hernias who present in early infancy with respiratory symptoms. Paralysis of the diaphragm due to phrenic nerve palsy recovers spontaneously in the majority of patients. The selective use of diaphragmatic plication for this condition is widely accepted, but the decision and appropriate timing for surgical intervention is often difficult. The results of surgery are very good both in the early postoperative period and also on long-term follow-up. The diagnosis of traumatic diaphragmatic hernia is often overlooked in the presence of other major injuries. The danger of strangulation of contents of this hernia is ever present and repair should be undertaken without delay once the diagnosis is made.
特殊类型的膈疝可分为两大类,即先天性和后天性。迟发性Bochdalek疝的诊断常常存在困难,可能导致治疗不当。典型的例子是疝入的胃被误诊为张力性气胸。绞窄是Bochdalek疝一种罕见但重要的并发症。文中描述了多种关闭大的膈肌缺损的技术,并推荐了那些能在危重症婴儿中迅速有效实施的手术方法。由于不同作者对膈膨升的定义不同,有关膈膨升的文献令人困惑。术前可能很难将这种情况与伴有囊袋的先天性膈疝区分开来。由于干预决策基于临床和影像学评估,这种区分通常并不重要。大多数Morgagni疝无症状,绞窄很少发生。有一小部分患有Morgagni疝的婴儿在婴儿早期出现呼吸道症状。膈神经麻痹导致的膈肌麻痹在大多数患者中可自发恢复。选择性地对这种情况使用膈肌折叠术已被广泛接受,但手术干预的决策和合适时机往往很难确定。手术结果在术后早期和长期随访中都非常好。创伤性膈疝的诊断在存在其他重大损伤时常常被忽视。这种疝内容物发生绞窄的风险始终存在,一旦确诊应立即进行修复。