Farronato Giampietro, Maspero Cinzia, Farronato Davide, Gioventù Silvia
Department of Orthodontics, University of Milan, Milan, Italy.
Angle Orthod. 2009 Jan;79(1):178-85. doi: 10.2319/111307-393.1.
Cleidocranial dysostosis is a rare congenital skeletal disorder, associated with clavicular hypoplasia or aplasia, delayed closure of cranial fontanels, brachycephalic skull, delayed exfoliation of primary dentition, eruption of permanent teeth, and multiple supernumerary and morphologic abnormalities of the maxilla and mandible. The disorder is caused by mutation in the CBFA1 gene, on the short arm of chromosome 6p21. The prevalence of cleidocranial dysostosis is estimated one per million, without sex or ethnic group predilection. The purpose of this paper is to describe the orthodontic treatment in a patient with cleidocranial dysostosis. Therapy may include removal of supernumerary teeth, surgical exposure of impacted teeth, and orthodontic treatment.
锁骨颅骨发育不全是一种罕见的先天性骨骼疾病,与锁骨发育不全或发育不全、颅囟闭合延迟、短头畸形颅骨、乳牙迟脱、恒牙萌出以及上颌骨和下颌骨多发多生牙和形态异常有关。该疾病由位于6号染色体短臂6p21上的CBFA1基因突变引起。锁骨颅骨发育不全的患病率估计为百万分之一,无性别或种族倾向。本文旨在描述一名锁骨颅骨发育不全患者的正畸治疗。治疗可能包括拔除多生牙、手术暴露阻生牙以及正畸治疗。