Mabrouk Yosra, Ammar Sinda, Labidi Amel, Mansour Lamia, Ghoul Sonia
Removable Prosthetics Department, ABCDF Laboratory (LR12ES10), Faculty of Dental Medicine, University of Monastir, Tunisia.
ABCDF Laboratory (LR12ES10), Faculty of Dental Medicine, University of Monastir, Tunisia.
Case Rep Dent. 2020 Dec 19;2020:8910798. doi: 10.1155/2020/8910798. eCollection 2020.
Cleidocranial dysplasia (CCD) is a rare inherited skeletal syndrome. There is no consensus regarding the dental treatment strategy. . To report a rare case of cleidocranial dysplasia and to summarize the current clinical and dental features and prosthetic treatment of similar CCD patients reported in the literature. . A 17-year-old girl was diagnosed with CCD. She had a short stature with the ability to bring the shoulders under the chest. All remaining teeth were deciduous except the four first molars were permanent. The maxilla was hypoplastic with a relative prognathism of the mandible. The cone-beam computed tomography examination showed a distorted and incomplete root formation of the permanent teeth. She was treated with both, complete and partial, removable overdentures. PubMed was used for the literature research using the following keys words "Cleidocranial Dysplasia"[Mesh], "Prosthodontics"[Mesh], "Dental Care"[Mesh], "cleidocranial dysostosis," and "dental treatment." The retention of deciduous teeth was described in the majority of cases. All the patients had supernumerary teeth. The most used treatments were dental prosthetics and orthodontics. The fixed prosthetic implant was the most used type of prosthetic treatment. Among the 15 cases who specified the type of prosthetic treatment, seven patients received removable dentures. Prosthetics was indicated especially for aged patients. . Removable prostheses are a good solution that rapidly restores esthetics and functions. The use of implants for these patients needs to be validated by a long-term follow-up.
锁骨颅骨发育不全（CCD）是一种罕见的遗传性骨骼综合征。关于牙科治疗策略尚无共识。报告一例罕见的锁骨颅骨发育不全病例，并总结文献中报道的类似CCD患者的当前临床和牙科特征及修复治疗情况。一名17岁女孩被诊断为CCD。她身材矮小，能够将双肩拉至胸前下方。除四颗第一恒磨牙外，其余牙齿均为乳牙。上颌发育不全，下颌相对前突。锥形束计算机断层扫描检查显示恒牙牙根形成扭曲且不完全。她接受了全口和局部可摘覆盖义齿治疗。使用PubMed进行文献研究，关键词为“锁骨颅骨发育不全”[医学主题词]、“口腔修复学”[医学主题词]、“牙科护理”[医学主题词]、“锁骨颅骨发育异常”和“牙科治疗”。大多数病例中都描述了乳牙滞留情况。所有患者均有多生牙。最常用的治疗方法是牙科修复和正畸。固定修复种植体是最常用的修复治疗类型。在15例明确修复治疗类型的病例中，7例患者接受了可摘义齿修复。修复治疗尤其适用于老年患者。可摘义齿是一种能迅速恢复美观和功能的良好解决方案。对于这些患者使用种植体需要通过长期随访来验证。
