Pires Fraga Murillo Francisco, Mello Daniel, Jorge Douglas, Perin Luis Fernando, Helene Américo
Plastic Surgery Discipline of the Surgery Department, Santa Casa de São Paulo, Faculty of Medical Sciences, São Paulo, Brazil.
J Plast Reconstr Aesthet Surg. 2009 Dec;62(12):e561-4. doi: 10.1016/j.bjps.2008.11.058. Epub 2009 Jan 4.
The congenital infiltrating lipomatosis (LCI) represents a distinct, clinical and pathological aspect of fat soft-tissue neoplasia; very few cases of which have been described in literature. In 1983, Slavin and Cols described the main characteristics of LCI as:(1) non-encapsulated tumours containing mature adipocites, (2) fat infiltration in muscles and adjacent soft parts, (3) absence of malignant characteristics, (4) absence of lipoblasts, (5) presence of fibrous elements, increased number of vessels and nerves and (6) adjacent bone hypertrophy. In this article, we describe a congenital infiltrating lipomatosis of the face in a child and discuss the diagnoses and the treatment of this disease.
先天性浸润性脂肪瘤病（LCI）是脂肪软组织肿瘤一种独特的临床和病理表现；文献中对此描述的病例极少。1983年，斯拉文及其同事将LCI的主要特征描述为：（1）包含成熟脂肪细胞的非包膜性肿瘤，（2）脂肪浸润至肌肉及相邻软组织，（3）无恶性特征，（4）无脂肪母细胞，（5）存在纤维成分、血管和神经数量增加，以及（6）相邻骨骼肥大。在本文中，我们描述了一名儿童面部的先天性浸润性脂肪瘤病，并讨论了该疾病的诊断和治疗。
