Xue T, Wei L, Qiao L, Zha D J, Chen X D, Qiu J H
Department of Otolaryngology, Xijing Hospital, Fourth Military Medical University, Xi'an, Shaanxi, PR China.
J Laryngol Otol. 2009 May;123(5):e16. doi: 10.1017/S0022215109004435. Epub 2009 Jan 21.
We report an extremely rare case of malignant triton tumour.
Case report and review of the world literature concerning malignant triton tumour and heredity.
We present the case of a 47-year-old woman who underwent a lateral rhinotomy surgical resection of a malignant triton tumour of the right paranasal sinuses, a rare location for this tumour. Thereafter, she received adjuvant radiotherapy. The prognosis for this group of tumours is poor. Radical surgical excision of the tumour followed by radiation therapy must be the treatment of choice.
To our knowledge, this is a rare report in the world literature of malignant triton tumour. This case indicates that malignant triton tumour of the paranasal sinuses is a rare disease which otolaryngologists should be aware of, and one which should be included in the differential diagnosis of malignant lesions involving the sinonasal tract.
我们报告一例极其罕见的恶性蝾螈瘤病例。
病例报告并回顾世界范围内有关恶性蝾螈瘤及遗传方面的文献。
我们呈现了一名47岁女性的病例，该患者接受了右侧鼻窦恶性蝾螈瘤的鼻侧切开术手术切除，此肿瘤的这一发病部位较为罕见。此后，她接受了辅助放疗。这类肿瘤的预后较差。肿瘤的根治性手术切除后再进行放射治疗必定是首选治疗方法。
据我们所知，这是世界文献中关于恶性蝾螈瘤的一份罕见报告。该病例表明鼻窦恶性蝾螈瘤是一种罕见疾病，耳鼻喉科医生应有所认识，且应将其纳入鼻窦道恶性病变的鉴别诊断中。
