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皮质基底节变性中的局灶性反射性肌阵挛

Focal reflex myoclonus in corticobasal degeneration.

作者信息

Carella F, Scaioli V, Franceschetti S, Girotti F, Giovannini P, Ciano C, Caraceni T

机构信息

Division of Neurology, National Neurologic Institute C. Besta, Milan, Italy.

出版信息

Funct Neurol. 1991 Apr-Jun;6(2):165-70.

PMID:1916457
Abstract

Focal reflex myoclonus was observed in a patient clinically diagnosed as affected by corticobasal degeneration. Myoclonus was not preceded by a cortical discharge and contralateral parietal components of the somatosensory evoked potentials were reduced in amplitude. No simple pathophysiological mechanism can account for all cases of focal reflex myoclonus seen in clinical practice.

摘要

在一名临床诊断为患有皮质基底节变性的患者中观察到局灶性反射性肌阵挛。肌阵挛之前没有皮质放电,体感诱发电位的对侧顶叶成分波幅降低。没有简单的病理生理机制可以解释临床实践中所见的所有局灶性反射性肌阵挛病例。

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