Carella F, Ciano C, Panzica F, Scaioli V
Division of Neurology, C. Besta National Neurological Institute, Milan, Italy.
Mov Disord. 1997 Jul;12(4):598-603. doi: 10.1002/mds.870120419.
Five patients with unilateral myoclonus and a clinical diagnosis of corticobasal degeneration (CBD) were studied. All patients showed enhanced long-loop responses in their myoclonic arms without enlarged somatosensory potentials. The cortical relay time of the long-loop responses was studied in three patients, in two of whom it was < 2 ms, even in the nonmyoclonic arm. Myoclonus in CBD is probably related to an enhanced long-loop reflex whose pathway is unlikely to be the same as that in classic cortical reflex myoclonus.
对5例单侧肌阵挛且临床诊断为皮质基底节变性（CBD）的患者进行了研究。所有患者在其肌阵挛侧上肢均表现出长环反应增强，而体感诱发电位未增大。对3例患者的长环反应的皮质中继时间进行了研究，其中2例患者的皮质中继时间<2毫秒，即使在非肌阵挛侧上肢也是如此。CBD中的肌阵挛可能与长环反射增强有关，其通路不太可能与经典皮质反射性肌阵挛相同。
