Lin Chen-Sung, Yu Yuan-Bin, Hsu Han-Shui, Chou Teh-Ying, Hsu Wen-Hu, Huang Biing-Shiun
Division of Thoracic Surgery, Department of Surgery, Keelung Hospital, Department of Health Executive Yuan, Keelung, Taipei, Taiwan, R.O.C.
J Chin Med Assoc. 2009 Jan;72(1):34-8. doi: 10.1016/S1726-4901(09)70017-6.
Both pure red cell aplasia (PRCA) and hypogammaglobulinemia are rarer conditions than myasthenia gravis (MG) in thymoma patients. Several articles have discussed the relation between PRCA and thymoma or hypogammaglobulinemia and thymoma, and their proper treatments. Instances of both PRCA and hypogammaglobulinemia in a thymoma patient are few and reported sporadically in the literature. We discuss a 46-year-old woman with thymoma and simultaneous PRCA and hypogammaglobulinemia who achieved complete remission from PRCA after perioperative steroid administration and extended thymectomy, and review the literature.
在胸腺瘤患者中,纯红细胞再生障碍性贫血(PRCA)和低丙种球蛋白血症都比重症肌无力(MG)少见。已有多篇文章讨论了PRCA与胸腺瘤或低丙种球蛋白血症与胸腺瘤之间的关系及其合适的治疗方法。胸腺瘤患者同时出现PRCA和低丙种球蛋白血症的病例很少,且文献中多为零星报道。我们讨论了一名46岁患有胸腺瘤、同时合并PRCA和低丙种球蛋白血症的女性患者,该患者在围手术期给予类固醇并扩大胸腺切除术后PRCA完全缓解,并对相关文献进行了综述。